The members of the Korean Association of Pediatric Surgeons conducted a retrospective study of two hundred and twenty-two cases of intestinal atresia for the period from January 1, 2007 to December 31, 2009. Seventeen hospitals were involved. There were 76 duodenal, 65 jejunal, and 81 ileal atresias (3 colonic). The male to female ratio was 0.85:1 in DA and 1.34:1 in JIA. Ninety-four patients(43.3%) were premature babies (DA 40.3%, JA 64.6%, IA 28.8%), and 70 babies (32.0%) had low birth weight (DA 38.7%, JA 44.4%, IA 16.0%). Antenatal diagnosis was made in 153 cases (68.9%). However, 27 infants (17.6%) with antenatal diagnosis were transferred to the pediatric surgeon's hospitals after delivery. Maternal polyhydramnios was observed in 81 cases (36.59%) and most frequent with proximal obstruction. In forty-four cases (19.8%), only simple abdominal film was taken for diagnostic study. The associated malformations were more frequently observed in DA - 61.8% in DA and 22.6% in JIA. Meconium peritonitis, small bowel volvulus and intussusception were more frequently associated with ileal atresia. The overall mortality rate was 3.6%.