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Review Article

Congenital Esophageal Stenosis in Children: From Etiology to Prognosis

Soo-Hong Kim1, Hyun-Young Kim2
Journal of the Korean Association of Pediatric Surgeons 2018;24(1):1-4.
Published online: June 30, 2018

1Department of Pediatric Surgery, Pusan National University Children's Hospital, Yangsan, Korea.

2Department of Pediatric Surgery, Seoul National University Children's Hospital, Seoul, Korea.

Correspondence: Hyun-Young Kim. Department of Pediatric Surgery, Seoul National University Children's Hospital, 101 Daehak-ro, Jongno-gu, Seoul 03080, Korea. Tel: +82-2-2072-2478, Fax: +82-2-747-5130, spkhy02@snu.ac.kr
• Received: March 5, 2018   • Accepted: April 13, 2018

Copyright © 2018 Korean Association of Pediatric Surgeons

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (https://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

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  • Congenital esophageal stenosis (CES) is a rare disease that has been reported to occur once in every 25,000 to 50,000 births. According to its etiology, CES is divided into 3 subtypes, tracheobronchial remnants (TBR), fibromuscular hypertrophy (FMH) and membranous diaphragm (MD). Symptoms begin at the weaning period and the introduction of solid food around 6 months with dysphagia and vomiting. Esophagography is first screening test and endoscopic ultrasonography plays important roles to diagnose subtypes deciding therapeutic plan. TBRs were generally treated with surgical resection and end-to-end anasotomosis, whereas FMH and MD had good response rate to endoscopic or radiologic guided dilatation. This article reviews the literature on the etiology, clinical course, diagnosis and management of CES including recent opinion.
  • Keywords: Congenital esophageal stenosis; Esophagus; Tracheobronchial remnants; Child

No potential conflict of interest relevant to this article was reported.

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Fig. 1

Histologic findings of the resected congenital esophageal stenosis segment revealed respiratory epithelium (arrows) and cartilage (arrowheads) in the esophageal wall (H&E, ×40).

jkaps-24-1-g001.jpg
Fig. 2

Upper gastrointestinal contrast study revealed a dilated esophagus proximal to a distal esophageal stenosis (arrows). (A) Anteroposterior view. (B) Lateral view.

jkaps-24-1-g002.jpg
Fig. 3

Endoscopic ultrasound revealed hypoechoic structure in the esophageal wall. Data from the article of Quiros et al. (J Pediatr Gastroenterol Nutr 2013;56:e14) [18].

jkaps-24-1-g003.jpg

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Congenital Esophageal Stenosis in Children: From Etiology to Prognosis
J Korean Assoc Pediatr Surg. 2018;24(1):1-4.   Published online June 30, 2018
DOI: https://doi.org/10.13029/jkaps.2018.24.1.1
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Download a citation file in RIS format that can be imported by all major citation management software, including EndNote, ProCite, RefWorks, and Reference Manager.
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Congenital Esophageal Stenosis in Children: From Etiology to Prognosis
J Korean Assoc Pediatr Surg. 2018;24(1):1-4.   Published online June 30, 2018
DOI: https://doi.org/10.13029/jkaps.2018.24.1.1
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Congenital Esophageal Stenosis in Children: From Etiology to Prognosis
Image Image Image
Fig. 1 Histologic findings of the resected congenital esophageal stenosis segment revealed respiratory epithelium (arrows) and cartilage (arrowheads) in the esophageal wall (H&E, ×40).
Fig. 2 Upper gastrointestinal contrast study revealed a dilated esophagus proximal to a distal esophageal stenosis (arrows). (A) Anteroposterior view. (B) Lateral view.
Fig. 3 Endoscopic ultrasound revealed hypoechoic structure in the esophageal wall. Data from the article of Quiros et al. (J Pediatr Gastroenterol Nutr 2013;56:e14) [18].

Fig. 1

Fig. 2

Fig. 3

Congenital Esophageal Stenosis in Children: From Etiology to Prognosis
APS : Advances in Pediatric Surgery

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