Advances in Pediatric Surgery

[English]

Familial Isolated Anorectal Malformation: A Case Report: Jinyoung Park; J Korean Assoc Pediatr Surg 2017;23(1):12-14. Published online June 26, 2017; DOI: https://doi.org/10.13029/jkaps.2017.23.1.12

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There have been a few reports of familial anorectal malformations extending over more than one generation. We experienced a case of a family with 3 members spanning 2 generations affected with isolated low type anorectal malformations. They had same low type of anorectal malformations. In all 3 patients, a perianal anoplasty was performed.

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[English]

Inguinal Ectopic Scrotum, Anorectal Malformation with Sacral Agenesis and Limb Defects: An Unusual Presentation: Monika Bawa, Saurabh Garge, Virender Sekhon, KLN Rao; J Korean Assoc Pediatr Surg 2015;21(2):32-34. Published online December 22, 2015; DOI: https://doi.org/10.13029/jkaps.2015.21.2.32

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A case of congenital ectopic scrotum in neonatal period is described. The ectopic scrotum was located in the right inguinal area and the left hemiscrotum was found in normal location and each hemi-scrotum contained their testis. The neonate also had imperforate anus as low anorectal malformation with spinal abnormalities (hemi-sacrum and hemi-pelvis), right knee flexion contracture and right club foot. The embryological explanation in the literature of ectopic scrotum and its associated anomalies is discussed.

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[English]

Introduction of Anorectal Malformations: Kwi Won Park; J Korean Assoc Pediatr Surg 2006;12(1):86-90. Published online June 30, 2006; DOI: https://doi.org/10.13029/jkaps.2006.12.1.86

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History, incidence and associated anormalies of the anorectal malformations were reviewed.

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[English]

A Comparative Study of Two National Surveys of Anorectal Malformations in the Korean Association of Pediatric Surgeons: Park, Jinyoung , Kim, Woo Ki , Kim, In Koo , Kim, Jae Eok , Kim, Jae Chun , Kim, Hyun Hak , Kim, Sang Youn , Kim, Dae Yeon , Kim, Seong Chul , Kim, Chong Suk , Kim, Hyun-Young , Nam, So Hyun , Park, Kwi-Won , Park, Woo Hyun , Boo, Yoon Jung , Song, Young Tack , Oh, Soo Myung , Yoo, Soo Young , Lee, Doo Sun , Seo, Jeong-Meen , Oh, Jung-Tak , Lee, Nam-Hyuk , Lee, Myung-Duk , Lee, Suk-Koo , Lee, Seong Cheol , Lee, Jong In , Chang, Soo Il , Chung, Sang Young , Chang, Hye Kyung , Jung, Sung Eun , Jeong, Yeon Jun , Chung, Jae Hee , Chung, Eul Sam , Jung, Poong Man , Cho, Ma Hae , Choi, Kum Ja , Choi, Soon Ok , Choi, Seung Hoon , Choe, Yun Mee , Han, Seok Joo , Huh, Young Soo , Hong, Jeong , Hwang, Eui Ho; Adv Pediatr Surg 2022;28(2):37-46.; DOI: https://doi.org/10.13029/aps.2022.28.2.37

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Purpose
Anorectal malformations (ARMs) represent a wide spectrum of anomalies with various presentations and associated anomalies. The management of ARMs is still controversial and various managements for ARMs have been proposed. The aim of this study was to identify the status of ARMs in Korea and to analyze the data regarding classification, treatment and functional outcomes of ARMs among the Korean Association of Pediatric Surgeons (KAPS) members.
Methods
The KAPS has conducted a national survey for ARMs in 1999 and 2015 to analyze the differences and changes in the classification, treatment, and functional outcomes of ARMs.
Results
A total of 295 and 619 ARMs patients were enrolled in the second and third national survey, respectively. The most common type among male and female was the low type in the second national survey and low defects (cutaneous fistula, anal stenosis, membrane) in the third national survey. Most common associated anomalies were genitourinary system in the second national survey and cardiovascular system in the third national survey. Various surgical options including anoplasty, posterior sagittal anorectoplasty (PSARP) and laparoscopic surgery with or without colostomy were performed. Unfortunately, comparison regarding functional outcomes between 2 national surveys was not possible due to the use of different classification and functional assessment criteria.
Conclusion
We suggest making an ARMs registry at a national level so that multicenter functional outcome data can be collected for a better understanding and management of this rare anomaly.